ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA - CASE REPORT FROM PAKISTAN AND REVIEW OF LITERATURE

Abstract

Arrhythmogenic right ventricular dysplasia (ARVD)
is disorder of cardiac muscle characterized by the
replacement of myocytes by fibrofatty tissue and
extracellular matrix.ARVD is a genetic cardiomyopathy characterized by
fibrous-adipose substitution of the right (6) and rarely
of the left ventricular myocardium (7).An important focus of
the evaluation of a patient diagnosed with ARVD is to
identify those at risk for SCD.ARVD is a rare disorder with a very
heterogenous presentation. The disease is frequently
asymptomatic until adolescence and the findings on
testing are subtle - hence frequently missed.