Hypertrophic Cardiomyopathy Involving Right Ventricle-Clinical, Hemodynamic And Angiographic Findings

Abstract

A case of fifteen months old child presented with clinical picture suggestive of RVOT obstruction was diagnosed to have HCM involving Right Ventricle. The child also had associated unusual congenital anomalies like cleft palate and congenital bilateral talipes equinovarus. Hypertrophic Cardiomyopathy (HCM) involves ventricular septum and frequently left & right vent ricular free walls. Fifteen per cent patients with typical clinical and hemodynamic features of HCM show systolic gradients across right ventricular outf low tract. It is rare to find right ventricular inv olvement in absence of pressure gradient across left ventricular outflow tract. The case reported here has unusual features as it is presented at very early age of 8 months; associated with unusual anomalies like cleft palate, bilateral talipes equinovarus and has documented isolated RVOT gradient in absence of LVOT gradient.