Arrhythmogenic Right Ventricular Dysplasia With Epsilon Potential Case Report With Review

Abstract

Summary:
Arrhythmogenic right ventricular dysplasia is a form of cardiomyopathy which causes life threatening ventricular tachyarrhythmia in adults. We present a case who ultimately expired along with review of literature of this entity.

Discussion:
Arrhythmogenic right ventricular dysplasia (ARVD) was first described by Fontaine et al in i977. It is a clinical entity characterized by episodes of ventricular tachycardia with a QRS configuration that is typical of a left ventricular delay, the presence of ventricular post excitation waves and global or regional wall motion abnormalities of the right ventricle4. The right ventricular muscle is partially or totally replaced by adipose and fibrous tissues8.